Diagnosis of arrhythmogenic right ventricular cardiomyopathy.

Arrhythmogenic right ventricular cardiomyopathy: diagnosis, prognosis, and treatment.

Arrhythmogenic right ventricular cardiomyopathy in a 52-year-old man – clinical presentation mimicking an acute coronary syndrome

Arrhythmogenic right ventricular cardiomyopathy is an infrequently diagnosed, genetically determined disease that leads to significant clinical consequences, including progressive heart failure and ventricular arrhythmias accounting for sudden cardiac death. We report the case of a 52-year-old patient who presented with ventricular tachycardia and features of an acute coronary syndrome. However...

MRI in childhood Arrhythmogenic Right Ventricular Cardiomyopathy and proposed modification of the Task Force Criteria for children

Background ARVC is a genetically determined cardiomyopathy which typically manifests clinically during the second to fourth decade of life. The diagnosis is made using a scoring system of signs and symptoms, known as the revised task force criteria (rTFC). MRI has recently been shown to be of little added value in the diagnosis of ARVC in adults. Its role in the pediatric age group is unclear. ...

Contribution of electroanatomical mapping to the diagnosis of arrhythmogenic right ventricular cardiomyopathy in a patient with sustained ventricular tachycardia.

Arrhythmogenic right ventricular cardiomyopathy (ARVC) is a primary cardiomyopathy, characterized mainly by anatomic and functional defects of the right ventricle. In many cases its diagnosis is quite difficult in spite of the existence of defined diagnostic criteria for the disease. We describe an interesting case of a patient with sustained ventricular tachycardia derived from the right ventr...

Arrhythmogenic Noncompaction Cardiomyopathy: Is There an Echocardiographic Phenotypic Overlap of Two Distinct Cardiomyopathies?

The clinical diagnosis of right ventricular (RV) cardiomyopathies is often challenging. It is difficult to differentiate the isolated left ventricular (LV) noncompaction cardiomyopathy (NC) from biventricular NC or from coexisting arrhythmogenic ventricular cardiomyopathy (AC). There are currently few established morphologic criteria for the diagnosis other than RV dilation and presence of exce...

Arrhythmogenic right ventricular cardiomyopathy: contribution of different electrocardiographic techniques.

Arrhythmogenic right ventricular cardiomyopathy, also known as arrhythmogenic right ventricular dysplasia, is a condition in which myocardium is replaced by fibrous or fibrofatty tissue, predominantly in the right ventricle. It is clinically characterized by potentially lethal ventricular arrhythmias, and is a leading cause of sudden cardiac death. Its prevalence is not known exactly but is est...